Hereditary Hearing Loss Explained

Not all hearing loss comes as a result of ageing or noise. Some people are born with it. Not all hereditary or genetic hearing loss presents itself at birth. For those with hereditary hearing loss, it can develop at a later time or they might just be predisposed to develop a problem hearing.

How Common is Hereditary Hearing Loss?

Wikipedia details how common hereditary hearing loss is.

  • About 75 – 80% of inherited hearing loss is in recessive genes. This is called non-syndromic hearing impairment.
  • 20 – 25% of inherited hearing loss is from dominant genes. This is called syndromic hearing impairment. It means that the hearing loss is attributed to other clinical abnormalities.
  • Only 1 -2% of inherited hearing loss is inherited by X-linked patterns.
  • Less than 1% is from a mitochondrial inheritance.

Types of Hereditary Hearing Loss

Hereditary hearing loss can be caused by a genetic mutation. Some genetic mutations can interfere with the hair cells of the inner ear which are responsible for hearing. Not all gene mutations cause immediate hearing loss or deafness. In many cases, it does not present a problem until later in life. Scientists are studying gene mapping to help with diagnosis, research, treatment and a cure.

Hereditary hearing loss can also be a side effect of certain conditions including:

  • Otosclerosis
  • Usher’s Syndrome
  • Pendred Syndrome

Audiology Clinic Specializes in Solutions for Hearing Loss

At Audiology Clinic, we are here to help you through hearing loss. For more information, contact us today and schedule an appointment. We are here for you and work to meet your specific listening needs.